Paraneoplastic autoimmune multiorgan syndrome (paraneoplastic pemphigus) with unusual manifestations and without detectable autoantibodies. [caso clínico]
Por: Sanz Bueno, Jimena [Dermatología Médico-Quirúrgica y Venereología] | Cullen, Daniella [Dermatología Médico-Quirúrgica y Venereología] | Zarco Olivo, Carlos [Dermatología Médico-Quirúrgica y Venereología] | Vanaclocha Sebastián, Francisco [Dermatología Médico Quirúrgica y Venereología].
Colaborador(es): Servicio de Dermatología Médico-Quirúrgica y Venereología.
Tipo de material: ArtículoEditor: Indian journal of dermatology, venereology and leprology 2014Descripción: 80(4):328-30.Recursos en línea: Solicitar documento Resumen: We describe a patient with paraneoplastic autoimmune multiorgan syndrome (PAMS) secondary to a lymphoblastic T- cell lymphoma who presented with a lichenoid dermatitis and vitiligo, later developing bronchiolitis obliterans and autoimmune hepatitis. Notably, he had no detectable autoantibodies. The development of vitiligo and autoimmune hepatic involvement probably indicate a role for cytotoxic T- cell lymphocytes in the pathogenesis of this syndrome.Tipo de ítem | Ubicación actual | Signatura | Estado | Fecha de vencimiento |
---|---|---|---|---|
Caso clínico | PC16449 (Navegar estantería) | Disponible |
Formato Vancouver:
Sanz Bueno J, Cullen D, Zarco C, Vanaclocha F. Paraneoplastic autoimmune multiorgan syndrome (paraneoplastic pemphigus) with unusual manifestations and without detectable autoantibodies. Indian J Dermatol Venereol Leprol. 2014 Jul-Aug;80(4):328-30.
PMID: 25035358
Contiene 9 referencias
We describe a patient with paraneoplastic autoimmune multiorgan syndrome (PAMS) secondary to a lymphoblastic T- cell lymphoma who presented with a lichenoid dermatitis and vitiligo, later developing bronchiolitis obliterans and autoimmune hepatitis. Notably, he had no detectable autoantibodies. The development of vitiligo and autoimmune hepatic involvement probably indicate a role for cytotoxic T- cell lymphocytes in the pathogenesis of this syndrome.
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